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Intravascular lymphoma in a patient with systemic lupus erythematosus: a case reportUnidad de Enfermedades Autoinmunes Sistémicas, Hospital Clínico San Cecilio, Granada, Spain, danisanchezcano{at}supercable.es
Unidad de Enfermedades Autoinmunes Sistémicas, Hospital Clínico San Cecilio, Granada, Spain
Servicio de Dermatología, Hospital Clínico San Cecilio, Granada, Spain
Servicio de Anatomía Patológica, Hospital Clínico San Cecilio, Granada, Spain
Unidad de Enfermedades Autoinmunes Sistémicas, Hospital Clínico San Cecilio, Granada, Spain Intravascular lymphoma IVL is a rare and aggressive disorder characterized by proliferation of large lymphoid cells (most commonly B-cells) within the lumen of small vessels of nearly every organ. Obliteration of vessels leads to the different clinical signs, being cutaneous lesions and neurological signs the most frequent presentations, whereas lymph node and reticuloendothelial system involvement is typically absent.1—4 No association with SLE has been described up to the present. We report a case of IVL in a patient with systemic lupus erythematosus (SLE) involving skin, central nervous system (CNS) and bone marrow. Lupus (2007) 16, 525—528.
Key Words: B-cell lymphoma intravascular lymphoma systemic lupus erythematosus
Lupus, Vol. 16, No. 7,
525-528 (2007) This article has been cited by other articles:
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