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Childhood vasculitisGreat Ormond Street Hospital for Children, Great Ormond Street, London WC1N 3JH, UK Vasculitis can and does occur in childhood. Apart from the relatively common vasculitides (HenochSchönlein purpura, Kawasaki disease and in world wide terms Takayasu disease) there are a number of important but comparatively rare disorders affecting children. These include macroscopic and microscopic polyarteritis, cutaneous polyarteritis, Wegener's granulomatosis, ChurgStrauss syndrome, primary angiitis of the central nervous system, hypersensitivity angiitis, hypocomplimentaemic urticarial vasculitis, vasculitis associated with various connective tissue disorders and vasculitis associated with conditions such as Behçets syndrome, familial Mediterranean fever and Cogan's syndrome. Distinguishing these conditions from other disorders is often difficult and requires clinical acumen and appropriate investigative procedures. With modern therapeutic agents, it is possible to implement appropriate therapy but in spite of this, there remains a not inconsequential morbidity and mortality.
Key Words: childhood vasculitis polyarteritis Kawasaki disease Wegener's granulomatosis HenochSchönlein purpura
Lupus, Vol. 7, No. 4,
259-265 (1998) This article has been cited by other articles:
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